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Validated Risk Stratification for RYR2-Mediated Catecholaminergic Polymorphic Ventricular Tachycardia on Beta-Blocker Therapy
Cardiologyrisk stratificationCPVT

Validated Risk Stratification for RYR2-Mediated Catecholaminergic Polymorphic Ventricular Tachycardia on Beta-Blocker Therapy

By MedXY|Sep 6, 2026

This article reviews a validated clinical risk model predicting arrhythmic events in patients with RYR2-mediated CPVT receiving beta-blockers, facilitating personalized management to reduce life-threatening arrhythmias.

Clinical Diagnosis of Calcium Release Deficiency Syndrome in a Family With Sudden Cardiac Death
Cardiologyarrhythmia diagnosis
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calcium release deficiency syndrome

Clinical Diagnosis of Calcium Release Deficiency Syndrome in a Family With Sudden Cardiac Death

By MedXY|Jul 10, 2026

A 5-generation French Canadian family with history of sudden cardiac death was diagnosed with calcium release deficiency syndrome using a novel burst pacing provocation test, illustrating its clinical utility and highlighting the importance

Precision Risk Assessment in CPVT: New Validated Models Predict Arrhythmic Events on Beta-Blocker Therapy
CardiologyCardiologyCPVT

Precision Risk Assessment in CPVT: New Validated Models Predict Arrhythmic Events on Beta-Blocker Therapy

By MedXY|Jan 3, 2026

A landmark study has developed and validated the first clinical risk prediction models for RYR2-mediated CPVT, identifying key factors like age at treatment and prior symptoms that determine life-threatening outcomes despite beta-blocker th

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